Clinical case: allogeneic transplantation of hematopoietic stem cells for Fanconi anemia in the onset of refractory anemia with excess blasts

نویسندگان

چکیده

Fanconi anemia (AF) is a hereditary genetic disease characterized by developmental abnormalities, progressive bone marrow failure, hypersensitivity to alkylating agents, and tendency hematological solid tumors throughout life. The only curative option in the treatment of failure patients with AF allogeneic hematopoietic stem cell transplantation (allo-HSCT). There are no detailed descriptions allo-HSCT Russian-language literature. On example clinical case at onset myelodysplastic syndrome, choose method for treating presented.

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ژورنال

عنوان ژورنال: Rossijskij žurnal detskoj gematologii i onkologii

سال: 2023

ISSN: ['2413-5496', '2311-1267']

DOI: https://doi.org/10.21682/2311-1267-2022-9-4-114-118